From
Colorectal Channel
Colorectal Quiz Episode 13: Newborn ARM Part 2
With Dr. Jason Frischer & Dr. Marc Levitt · hosted by Dr. Amanda Jensen & Dr. Rod Gerardo
Chapter 1 of 6 · Fundamentals
Introduction
Introduction and episode context
Expert statements on this page
No expert statements were drawn from this page.
Host summaries · secondary, not cited in answers
Educational content from recorded physician discussions — not medical advice. Talk to your (or your child's) care team about your situation.
Video
Anorectal Malformation Management of Female Patients Part I: Pediatric...
26 min · Published Apr 2012
Video
Pediatric Colorectal Contraversies Part I: Pediatric Colorectal Contraversies...
Dr. Todd Ponsky · 25 min · Published Aug 2017
Podcast
Colorectal Quiz 25: Perineal Groove
30 min · Published Jan 2022
Podcast
Colorectal Quiz Episode 14: ARM Newborn Part 3
10 min · Published Jun 2021
Video
Surgical Management Of Female Anorectal Malformation Patients Including...
57 min · Published Nov 2018
Podcast
Colorectal Quiz Episode 28: Female ARM Management - Perineal Fistula
19 min · Published Feb 2022
Video
Validation of an anorectal malformation trainer - Can a high-fidelity model simulate real life?
1 min · Published Jun 2026
Video
Complications and Long-Term Outcomes of Patients With Cloacal Malformation After Bowel Neovagina...
1 min · Published Jun 2026
Video
Safety and utility of long-acting steroid injection for management of post-operative stricture...
1 min · Published Jun 2026
Video
Association Between Social Determinants of Health and Choice of Urinary Reconstruction in Children
1 min · Published Jun 2026
Video
The Perineal Body Preserving PSARP (PPP)
11 min · Published Jun 2026
Video
Update Course Rewind 2025: Hirschsprung + ARM: Rare but Real
1 min · Published May 2026
Podcast
Colorectal Quiz: Episode 47
Marc Levitt · 22 min · Published May 2025
Video
Colorectal Quiz: Episode 46 - Hirschsprung's Disease
Marc Levitt · 29 min · Published Apr 2025
Podcast
Colorectal Quiz: Episode 46
Marc Levitt · 29 min · Published Apr 2025
Video
Colorectal Quiz: Episode 44 - HD Frozen Section
Marc Levitt · 18 min · Published Feb 2025
Podcast
Colorectal Quiz: Episode 43
Marc Levitt · 23 min · Published Jan 2025
Video
Colorectal Quiz Episode 38: Transitional Care in Colorectal Surgery
25 min · Published Mar 2024
Podcast
Long-term obstetric and gynecologic care for patients with anorectal malformations
21 min · Published Sep 2026
Podcast
Post-pubertal gynecologic evaluation and management of patients with anorectal malformations
22 min · Published Sep 2026
Podcast
Pre-pubertal gynecologic evaluation and management of patients with anorectal malformations
23 min · Published Sep 2026
Podcast
Methods of gynecologic evaluation for patients with anorectal malformations
21 min · Published Sep 2026
Podcast
Gynecologic care in patients with anorectal malformations: A primer and call to action
18 min · Published Sep 2026
Podcast
Evaluation and Management of Postsurgical Patient With Hirschsprung Disease Neurogastroenterology & Motility Committee: Position Paper of North American Society of Pediatric Gastroenterology, Hepatology, and Nutrition (NASPGHAN)
17 min · Published Sep 2026
What the experts said
Indications for surgery in female ARM include: hole too small, hole not in center of sphincter, and inadequate perineal body
Perineal groove with mucosal lining will keratinize and look like normal perineal body over time
Surgical intervention for perineal groove is indicated only if secreting mucus, causing irritation, or developing ulcers
If anal opening is adequately sized, surrounded by sphincter, and has a perineal body (albeit short), no surgery is indicated
Short perineal body will grow over time and there is nothing to do about it surgically
If half the fistula is within sphincter complex and half outside, patient will leak stool because they cannot close the hole, making surgery worthy
Vestibular fistula is very common in females and needs formal repair with hole transposed to center of sphincter
For vestibular fistula diagnosed in newborn period, options are primary repair if baby is well, or allow stooling through fistula for couple months then elective repair without stoma
Patients diagnosed with vestibular fistula at 6-12 months who have dilated rectosigmoid need diversion as first step, then repair
Purpose of diversion in ARM repair is to avoid perineal body dehiscence
Cloaca presents with single perineal orifice and hypertrophied area around clitoral hood is typical, not ambiguous genitalia
Cloaca patients do not need endocrine workup or steroids and there is no question of gender assignment - they are female
Cloaca patients are still being misdiagnosed as ambiguous genitalia, with some babies not having proper gender assignment for one to two weeks
Key to perineal exam is to push down and flatten the perineal body to assess if it is normal
Normal anus is centered within sphincter, of adequate size, and perineal body is of normal length properly distanced from vestibule
To evaluate for vestibular fistula, pull labia towards examiner with both hands to visualize vaginal opening and urethra
Congenital perineal groove usually epithelializes on its own by age two
Perineal groove can be misdiagnosed as contact dermatitis, trauma, or sexual abuse
Three qualities to assess in anal location are: anal size, location (whether surrounded by sphincter), and perineal body size
Urogenital sinus plus normal anus is an endocrine problem, but no anus and urogenital sinus is a cloaca
Use Hagar dilators starting low and working up for accurate anal size measurement; do not use fingers because every surgeon has different size glove
Female ARM exam requires determining number of perineal orifices: three orifices means perineal or vestibular fistula; two orifices raises question of fistula presence, vaginal atresia, or rectovaginal fistula; one orifice is cloaca
